典型文献
Light chain cardiac amyloidosis in a nonagenarian
文献摘要:
Cardiac amyloidosis is an infiltrative and restrictive cardiomyopathy caused by the extracellular deposition of amyloid fibrils within the heart as systemic amyloidosis, leading to heart failure, reduced quality of life, and death.[1]There are two major amyloid fibril proteins that affect the heart: amyloid immunoglobulin light chain (AL) and amyloid transthyretin (ATTR). The latter is further subdivided into wild-type ATTR and variant types based on the presence of a mutation in the transthyretin gene.
文献关键词:
中图分类号:
作者姓名:
Koji Takahashi;Mina Yamashita;Tomoki Sakaue;Daijiro Enomoto;Shigeki Uemura;Takafumi Okura;Shuntaro Ikeda;Takanori Senba;Akira Saijo;Nobuhisa Yamamura;Sohei Kitazawa
作者机构:
Department of Community Emergency Medicine,Ehime University Graduate School of Medicine,Ehime,Japan;Department of Cardiology,Yawatahama City General Hospital,Ehime,Japan;Department of Hematology,Yawatahama City General Hospital,Ehime,Japan;Department of Clinical Pathology,Yawatahama City General Hospital,Ehime,Japan;Department of Molecular Pathology,Ehime University Graduate School of Medicine,Ehime,Japan
文献出处:
引用格式:
[1]Koji Takahashi;Mina Yamashita;Tomoki Sakaue;Daijiro Enomoto;Shigeki Uemura;Takafumi Okura;Shuntaro Ikeda;Takanori Senba;Akira Saijo;Nobuhisa Yamamura;Sohei Kitazawa-.Light chain cardiac amyloidosis in a nonagenarian)[J].老年心脏病学杂志(英文版),2022(01):83-89
A类:
nonagenarian,infiltrative
B类:
Light,chain,cardiac,amyloidosis,Cardiac,restrictive,cardiomyopathy,caused,by,extracellular,deposition,fibrils,within,heart,systemic,leading,failure,reduced,quality,life,death,There,are,two,major,proteins,that,affect,immunoglobulin,light,AL,transthyretin,ATTR,latter,further,subdivided,into,wild,variant,types,presence,mutation,gene
AB值:
0.582188
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机标中图分类号,由域田数据科技根据网络公开资料自动分析生成,仅供学习研究参考。