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典型文献
Renal Amyloidosis Secondary to ANCA-Associated Vasculitis: A Case Report
文献摘要:
Renal amyloidosis secondary to anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis is extremely rare. Here, we reported a 77-year-old woman with ANCA-associated vasculitis. Renal biopsy with Masson trichrome staining showed pauci-immune crescentic glomerulonephritis, and electron microscopy showed amyloid deposition in the mesangial area. Immunofluorescence revealed kappa light chain and lambda light chain negative. Bone marrow biopsy revealed no clonal plasma cell. Finally, she was diagnosed as ANCA-associated vasculitis with secondary renal amyloid A amyloidosis.
文献关键词:
作者姓名:
Xin He;Jianping Ning;Hui Xu;Gong Xiao;Huixiang Yang;Weiyuan Wang;Xiaoying Wu;Hongling Yin;Xiaozhao Li
作者机构:
Department of Gastroenterology,Xiangya Hospital,Central South University,Changsha 410008,China;Department of Nephrology,Xiangya Hospital,Central South University,Changsha 410008,China;Department of Pathology,Xiangya Hospital,Central South University,Changsha 410008,China
引用格式:
[1]Xin He;Jianping Ning;Hui Xu;Gong Xiao;Huixiang Yang;Weiyuan Wang;Xiaoying Wu;Hongling Yin;Xiaozhao Li-.Renal Amyloidosis Secondary to ANCA-Associated Vasculitis: A Case Report)[J].中国医学科学杂志(英文版),2022(04):359-362
A类:
Vasculitis,pauci,crescentic
B类:
Renal,Amyloidosis,Secondary,ANCA,Associated,Case,Report,amyloidosis,secondary,neutrophil,cytoplasmic,antibody,associated,vasculitis,extremely,rare,Here,reported,year,old,woman,biopsy,Masson,trichrome,staining,showed,immune,glomerulonephritis,electron,microscopy,deposition,mesangial,area,Immunofluorescence,revealed,kappa,light,chain,lambda,negative,Bone,marrow,clonal,plasma,cell,Finally,she,was,diagnosed,renal
AB值:
0.616548
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